| Chemical Properties | Back Directory | [storage temp. ]
-20°C | [solubility ]
DMF: 15mg/mL,DMSO: 20mg/mL,Ethanol: 25mg/mL,PBS (pH 7.2): 10mg/mL | [form ]
A solid | [color ]
White to off-white |
| Hazard Information | Back Directory | [Biological Activity]
Isovaleryl-DL-carnitine-d9 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine . Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of metabolism characterized by a deficiency in isovaleryl-CoA dehydrogenase.1 | [References]
1.Rinaldo, P., Cowan, T.M., and Matern, D.Acylcarnitine profile analysisGenet.Med.10(2)151-156(2008)
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