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3-butanoyloxy-4-trimethylammonio-butanoate

CAS No.
25576-40-3
Chemical Name:
3-butanoyloxy-4-trimethylammonio-butanoate
Synonyms
Butyrylcarnitine;Butyrylcarnitine29;Butyryl-L-carnitine;R-Butyryl Carnitine;O-butanoyl-L-carnitine;n-Butyryl-L(-)-carnitine;L-Carnitine butyryl ester;Butyryl-L-carnitine >=97.0% (TLC);3-butanoyloxy-4-trimethylammonio-butanoate;(3R)-3-butanoyloxy-4-trimethylammonio-butanoate
CBNumber:
CB71235723
Molecular Formula:
C11H21NO4
Molecular Weight:
231.29
MDL Number:
MFCD01674827
MOL File:
25576-40-3.mol
MSDS File:
SDS
Last updated:2023-05-18 11:31:01

3-butanoyloxy-4-trimethylammonio-butanoate Properties

storage temp. 2-8°C
solubility soluble in Methanol, Water
form Solid
color White
optical activity [α]/D -23±2°, c = 1 in H2O

3-butanoyloxy-4-trimethylammonio-butanoate price More Price(7)

Manufacturer Product number Product description CAS number Packaging Price Updated Buy
Sigma-Aldrich 42623 Butyryl-L-carnitine ≥97.0% (TLC) 25576-40-3 10MG $90.4 2023-06-20 Buy
Sigma-Aldrich 42623 Butyryl-L-carnitine ≥97.0% (TLC) 25576-40-3 50MG $357 2023-06-20 Buy
Sigma-Aldrich 08984 Butyryl-L-carnitine analytical standard 25576-40-3 10MG $111 2022-05-15 Buy
ChemScene CS-0062329 Butyrylcarnitine >99.0% 25576-40-3 5mg $150 2021-12-16 Buy
ChemScene CS-0062329 Butyrylcarnitine >99.0% 25576-40-3 10mg $250 2021-12-16 Buy
Product number Packaging Price Buy
42623 10MG $90.4 Buy
42623 50MG $357 Buy
08984 10MG $111 Buy
CS-0062329 5mg $150 Buy
CS-0062329 10mg $250 Buy

3-butanoyloxy-4-trimethylammonio-butanoate Chemical Properties,Uses,Production

Uses

A potential prodrug, via the carnitine transporter OCTN2 and the amino acid transporter ATB0,+

Uses

Butyryl-L-carnitine may be used as an analytical reference standard for the separation and identification of underivatized butyryl-L-carnitine in human plasma samples using high-performance liquid chromatography coupled to tandem mass spectrometry (HPLC-MS/MS). It may also be used as an analytical reference standard for the quantification of the analyte in biological samples using chromatography-based techniques.

Definition

ChEBI: An optically active form of O-butanoylcarnitine having L-configuration.

General Description

Butyryl-L-carnitine is a naturally occurring compound belonging to the acylcarnitine class of compounds as listed in the human metabolome database (HMBD). These compounds are reported to be used as biomarkers in the diagnosis of carnitine deficiency. It acts as a carrier of long chain acyl groups from activated fatty acids across the inner mitochondrial membrane into the mitochondrial matrix where they undergo β-oxidation to acetyl CoA to obtain usable energy via the citric acid cycle.

Biochem/physiol Actions

Butyrylcarnitine is elevated in patients with Acyl-CoA dehydrogenase, short-chain (SCAD) deficiency, in infants with acute acidosis and generalized muscle weakness and in middle-aged patients with chronic myopathy localized in muscle; very long chain Acyl-CoA dehydrogenase deficiency, and celiac disease.

3-butanoyloxy-4-trimethylammonio-butanoate Preparation Products And Raw materials

Raw materials

Preparation Products

3-butanoyloxy-4-trimethylammonio-butanoate Suppliers

Global( 24)Suppliers
Supplier Tel Email Country ProdList Advantage
TargetMol Chemicals Inc.
+1-781-999-5354 +1-00000000000 marketing@targetmol.com United States 19892 58
Meike meditech (Foshan) Co.,Ltd
+86-0757-22239986 +86-18029359786 sales@mkmeditech.com China 1134 58
Aladdin Scientific
+1-+1(833)-552-7181 sales@aladdinsci.com United States 52927 58
ChemStrong Scientific Co.,Ltd 0755-0755-66853366 13670046396 sales@chem-strong.com China 18021 56
Sigma-Aldrich 021-61415566 800-8193336 orderCN@merckgroup.com China 51471 80
Beijing OKA biological technology co., LTD 010-010-010-62971590 18548936886 jack@oka-vip.com China 6897 58
ChemeGen(Shanghai) Biotechnology Co.,Ltd. 18818260767 sales@chemegen.com China 11289 58
ShangHai Anpel Co, Ltd. 18501792038; 18501792038 shanpel@anpel.com.cn China 9614 58
Energy Chemical 021-58432009 400-005-6266 marketing@energy-chemical.com China 44941 58
ChengDu SinoStandards Bio-Tech Co.,Ltd. , 028-83243028 19136088901 sinostandards@163.com China 4988 58
3-butanoyloxy-4-trimethylammonio-butanoate Butyrylcarnitine (3R)-3-butanoyloxy-4-trimethylammonio-butanoate (2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxobutoxy)-1-propanaminium Inner Salt Butyryl-L-carnitine L-Carnitine butyryl ester n-Butyryl-L(-)-carnitine R-Butyryl Carnitine O-butanoyl-L-carnitine Butyryl-L-carnitine >=97.0% (TLC) Butyrylcarnitine29 25576-40-3 Amino Acids 13C, 2H, 15N Amino Acids & Derivatives Chiral Reagents Intermediates & Fine Chemicals Pharmaceuticals