ANTI-NIEMANN-PICK C1

ANTI-NIEMANN-PICK C1 C화학적 특성, 용도, 생산

일반 설명

This gene encodes a large protein that resides in the limiting membrane of endosomes and lysosomes and mediates intracellular cholesterol trafficking via binding of cholesterol to its N-terminal domain. It is predicted to have a cytoplasmic C-terminus, 13 transmembrane domains, and 3 large loops in the lumen of the endosome - the last loop being at the N-terminus. This protein transports low-density lipoproteins to late endosomal/lysosomal compartments where they are hydrolized and released as free cholesterol. Defects in this gene cause Niemann-Pick type C disease, a rare autosomal recessive neurodegenerative disorder characterized by over accumulation of cholesterol and glycosphingolipids in late endosomal/lysosomal compartments

ANTI-NIEMANN-PICK C1 준비 용품 및 원자재

원자재

준비 용품

ANTI-NIEMANN-PICK C1 공급 업체

공급자	전화	이메일	국가	제품 수	이점
Xiamen Huijia Biological Technology Co., Ltd.	--		CHINA	6979	58
BEIJING BIOSYNTHESIS BIOTECHNOLOGY CO., LTD.	--	sales@bioss.com.cn	CHINA	6717	58
Xiamen Research Biotechnology Co., Ltd.	--	1562893815@qq.com	CHINA	6942	58
Shanghai Hao Zhun Biological Technology Co., Ltd.	--	info@zzsrm.com	CHINA	6846	58
Suzhou Ruinuode Biotechnology Co., Ltd.	--	2090855807@qq.com	CHINA	6063	58
Guangzhou Dongrui Technology Co., Ltd.	--	xiaoshan.wu@dr-tech.com.cn	CHINA	2839	58
Shanghai Beinuo Biotechnology Co., Ltd.	--	beinuobio@163.com	CHINA	6580	58
Beijing Qiangxin Borui Biotechnology Co., Ltd.	--	moumou@xxx.com	CHINA	2992	58
Riedel-de Haen AG	--		United States	6825	87
Zymed Laboratories Inc.	--		United States	3068	86