Глутароил карнитин химические свойства, назначение, производство
Химические свойства
Clear Thick Gel
Использование
A metabolite of L-Carnitine (C184110).
Биохимия/физиол Действия
Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.
Глутароил карнитин препаратная продукция и сырье
сырьё
препарат