Nitisinone химические свойства, назначение, производство
Описание
This reversible inhibitor of 4-hydroxyphenylpyruvate
dioxygenase was discovered by Swedish Orphan and is comarketed
by Apoteket AB and Rare Disease Therapeutics. It
is used as an adjunct to dietary restriction of tyrosine and
phenylalanine in the treatment of hereditary tyrosinemia type
1 (HT-1) disease.
Использование
Treatment of hereditary tyrosinemia.
Nitisinone препаратная продукция и сырье
сырьё
препарат