Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein

Anti-EXP,  Anti-KIAA0428,  Anti-Muscleblind-like  protein,  Anti-Triplet-expansion  RNA-binding  protein,  Anti-CUG  Triplet  Repeat  Expansion  Double-stranded  RNA-binding  protein Struktur
CAS-Nr.
Englisch Name:
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
Synonyma:
Monoclonal Anti-MBNL1 antibody produced in mouse;Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
CBNumber:
CB92093849
Summenformel:
Molgewicht:
0
MOL-Datei:
Mol file

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Eigenschaften

storage temp. 
-20°C

Sicherheit

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Chemische Eigenschaften,Einsatz,Produktion Methoden

Verwenden

Monoclonal Anti-MBNL1 antibody produced in mouse has been used in: immunoblotting, immunohistochemistry and immunocytochemistry

Allgemeine Beschreibung

Muscle blind-like 1 (MBNL1) is a homolog of human muscle blind like proteins. Proteins of the MBNL (muscleblind-like) family are mainly expressed in skeletal muscle neuronal tissues, thymus, liver and kidney.

Biochem/physiol Actions

Proteins of the MBNL (muscleblind-like) family enhance inclusion or exclusion of specific exons on different pre-mRNAs by inhibiting the activity of CUG-BP and ETR-3-like factors (CELF proteins) bound to distinct intronic sites. MBNL1 may be implicated in the stimulation of muscle differentiation. Mice knockouts for the MBNL1 gene develop muscle, eye, and RNA splicing abnormalities that are characteristic of the neuromuscular disease myotonic dystrophy (DM) disease.

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Upstream-Materialien And Downstream Produkte

Upstream-Materialien

Downstream Produkte


Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Anbieter Lieferant Produzent Hersteller Vertrieb Händler.

Global( 2)Lieferanten
Firmenname Telefon E-Mail Land Produktkatalog Edge Rate
Riedel-de Haen AG --
United States 6825 87
SIGMA-RBI --
Switzerland 6913 91

  • Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
  • Monoclonal Anti-MBNL1 antibody produced in mouse
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