Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
- CAS No.
- Chemical Name:
- Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
- Synonyms
- Monoclonal Anti-MBNL1 antibody produced in mouse;Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
- CBNumber:
- CB92093849
- Molecular Formula:
- Molecular Weight:
- 0
- MDL Number:
- MOL File:
- Mol file
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein price More Price(3)
Manufacturer | Product number | Product description | CAS number | Packaging | Price | Updated | Buy |
---|---|---|---|---|---|---|---|
Sigma-Aldrich | WH0004154M2 | Monoclonal Anti-MBNL1 antibody produced in mouse clone 3E7, purified immunoglobulin, buffered aqueous solution | 100μg | $524 | 2024-03-01 | Buy | |
Sigma-Aldrich | SAB1404054 | Monoclonal Anti-MBNL1 antibody produced in mouse clone 1D11, purified immunoglobulin, buffered aqueous solution | 100μg | $524 | 2024-03-01 | Buy | |
Sigma-Aldrich | M3320 | Monoclonal Anti-MBNL1 antibody produced in mouse ~1?mg/mL, clone HL 1822 (3A4-1E9), purified immunoglobulin, buffered aqueous solution | 100μL | $199.6 | 2024-03-01 | Buy |
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Chemical Properties,Uses,Production
Uses
Monoclonal Anti-MBNL1 antibody produced in mouse has been used in: immunoblotting, immunohistochemistry and immunocytochemistry
General Description
Muscle blind-like 1 (MBNL1) is a homolog of human muscle blind like proteins. Proteins of the MBNL (muscleblind-like) family are mainly expressed in skeletal muscle neuronal tissues, thymus, liver and kidney.
Biochem/physiol Actions
Proteins of the MBNL (muscleblind-like) family enhance inclusion or exclusion of specific exons on different pre-mRNAs by inhibiting the activity of CUG-BP and ETR-3-like factors (CELF proteins) bound to distinct intronic sites. MBNL1 may be implicated in the stimulation of muscle differentiation. Mice knockouts for the MBNL1 gene develop muscle, eye, and RNA splicing abnormalities that are characteristic of the neuromuscular disease myotonic dystrophy (DM) disease.
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Preparation Products And Raw materials
Raw materials
Preparation Products
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Suppliers
Supplier | Tel | Country | ProdList | Advantage | |
---|---|---|---|---|---|
Riedel-de Haen AG | -- | United States | 6825 | 87 | |
SIGMA-RBI | -- | Switzerland | 6913 | 91 |
Supplier | Advantage |
---|---|
Riedel-de Haen AG | 87 |
SIGMA-RBI | 91 |