Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein

CAS No.
Chemical Name:
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
Synonyms
Monoclonal Anti-MBNL1 antibody produced in mouse;Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein
CBNumber:
CB92093849
Molecular Formula:
Molecular Weight:
0
MDL Number:
MOL File:
Mol file

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Properties

storage temp. -20°C

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein price More Price(3)

Manufacturer Product number Product description CAS number Packaging Price Updated Buy
Sigma-Aldrich WH0004154M2 Monoclonal Anti-MBNL1 antibody produced in mouse clone 3E7, purified immunoglobulin, buffered aqueous solution 100μg $524 2024-03-01 Buy
Sigma-Aldrich SAB1404054 Monoclonal Anti-MBNL1 antibody produced in mouse clone 1D11, purified immunoglobulin, buffered aqueous solution 100μg $524 2024-03-01 Buy
Sigma-Aldrich M3320 Monoclonal Anti-MBNL1 antibody produced in mouse ~1?mg/mL, clone HL 1822 (3A4-1E9), purified immunoglobulin, buffered aqueous solution 100μL $199.6 2024-03-01 Buy
Product number Packaging Price Buy
WH0004154M2 100μg $524 Buy
SAB1404054 100μg $524 Buy
M3320 100μL $199.6 Buy

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Chemical Properties,Uses,Production

Uses

Monoclonal Anti-MBNL1 antibody produced in mouse has been used in: immunoblotting, immunohistochemistry and immunocytochemistry

General Description

Muscle blind-like 1 (MBNL1) is a homolog of human muscle blind like proteins. Proteins of the MBNL (muscleblind-like) family are mainly expressed in skeletal muscle neuronal tissues, thymus, liver and kidney.

Biochem/physiol Actions

Proteins of the MBNL (muscleblind-like) family enhance inclusion or exclusion of specific exons on different pre-mRNAs by inhibiting the activity of CUG-BP and ETR-3-like factors (CELF proteins) bound to distinct intronic sites. MBNL1 may be implicated in the stimulation of muscle differentiation. Mice knockouts for the MBNL1 gene develop muscle, eye, and RNA splicing abnormalities that are characteristic of the neuromuscular disease myotonic dystrophy (DM) disease.

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Preparation Products And Raw materials

Raw materials

Preparation Products

Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Suppliers

Global( 2)Suppliers
Supplier Tel Email Country ProdList Advantage
Riedel-de Haen AG -- United States 6825 87
SIGMA-RBI -- Switzerland 6913 91
Supplier Advantage
Riedel-de Haen AG 87
SIGMA-RBI 91
Anti-EXP, Anti-KIAA0428, Anti-Muscleblind-like protein, Anti-Triplet-expansion RNA-binding protein, Anti-CUG Triplet Repeat Expansion Double-stranded RNA-binding protein Monoclonal Anti-MBNL1 antibody produced in mouse